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Gene Model: Hao1

NomenclatureGenomic Location
SymbolHao1Chromosome1
NameHydroxyacid oxidase 1Linkage mapunknown
SpeciesDracomimus familiarisGenome CoordinatesChr1: 68 Mbp

Molecular Function

Has 2-hydroxyacid oxidase activity. Most active on the 2-carbon substrate glycolate, but is also active on 2-hydroxy fatty acids, with high activity towards 2-hydroxy palmitate and 2-hydroxy octanoate.

(S)-2-hydroxy acid + O2 = 2-oxo acid + H2O2.

Molecular Function Terms:

binding
   cofactor binding
      coenzyme binding
         FMN binding
   nucleotide binding
      FMN binding

catalytic activity
   oxidoreductase activity
      oxidoreductase activity, acting on CH-OH group of donors

Human Disease Association

No disease association.

Predicted Transcript
     1 ATGTCGGAAAAACCAATTTGCATTGCTGACTTTGAACACTATGCCAAGGCATTTCTTGGA
    61 AAATCTGTGTATGATTATTACAAATCCGGGGCTGATGAACAGCAAACACTGGCTGAAAAT
   121 GTCGCTGCCTTTTCAAGATTAAAATTATACCCCCGGATGTTGAAGGATGTGTCTTCCCTG
   181 GACCTGTCGACTTCAGTCTTGGGACAGAAGGTCAGCATGCCAATATGTGTCGCAGCAACT
   241 GCCATGCAGTGCATGGCTCATGCAGATGGGGAAATTGCTACTGTTAGAGCTTGCAGATCT
   301 ATGGGTACAGGAATGATGTTGAGTTCATGGGCCACATCATCAATAGAAGAAGTAGCTCAA
   361 GCAGCCCCAGAGGCAGTTCGATGGTTGCAGCTCTATATCTATAAGGACCGGGAGGTCACC
   421 AAATCTTTGGTGCGACGTGCAGAGAAAACTGGATACAAAGGCATCTTTGTGACTGTGGAC
   481 ACACCATTTCTTGGGAAGCGCTTAGATGATGTACGCAATAAGTTTCAGCTCCCACCACAT
   541 CTCAGGATGAAAAACTTTGAAACAAATGATTTGGCATTTTCATCTGAAAAAGGATATGGT
   601 GAAAACAGTGGCCTGTCTGTTTACGTTGCGGAAGCCATTGATCCCTCAATTAACTGGGAG
   661 GATATGAAGTGGCTCAGAGGACTGACTTCACTACCCATTGTTGCTAAAGGGATCATCAGA
   721 GCGGATGATGCTAGAGAAGCAGTGAAGCATGGTGTTAATGGGATTCTGGTGTCAAACCAT
   781 GGTGCACGTCAGTTGGATGGGGTTCCAGCTACTATTGAAATCCTACCTGAAATAATAGAA
   841 GCTGTGGAAGGAAAAATTGAGGTATTCCTTGATGGTGGCATACGAAAGGGCACAGATGTC
   901 CTCAAGGCTCTTGCCCTTGGAGCTAGAGCTGTGTTCTTGGGAAGACCTATCATCTGGGGA
   961 CTTGCTTATCAGGGTGAACAAGGTGTGAAGGAGGTTCTTCAGATATTGAAAGAAGAATTC
  1021 CACCTAGCAATGGCTCTCTCGGGCTGTCAGAGTGTGGAAGCAATAGACAGAACATTGGTA
  1081 CGGAGAGAGCAGTGGGCTGCCTCCAAGATGTAG

Predicted Protein Product
MSEKPICIADFEHYAKAFLGKSVYDYYKSGADEQQTLAENVAAFSRLKLYPRMLKDVSSL
DLSTSVLGQKVSMPICVAATAMQCMAHADGEIATVRACRSMGTGMMLSSWATSSIEEVAQ
AAPEAVRWLQLYIYKDREVTKSLVRRAEKTGYKGIFVTVDTPFLGKRLDDVRNKFQLPPH
LRMKNFETNDLAFSSEKGYGENSGLSVYVAEAIDPSINWEDMKWLRGLTSLPIVAKGIIR
ADDAREAVKHGVNGILVSNHGARQLDGVPATIEILPEIIEAVEGKIEVFLDGGIRKGTDV
LKALALGARAVFLGRPIIWGLAYQGEQGVKEVLQILKEEFHLAMALSGCQSVEAIDRTLV
RREQWAASKM
Protein Alignment to Mouse
sp|Q9WU19|HAOX1_MOUSE Hydroxyacid oxidase 1 OS=Mus musculus GN=Hao1 PE=2 SV=1
      MGI:96011 Hao1 hydroxyacid oxidase 1, liver (Chr 2)
        Length = 370

 Score = 1452 (516.2 bits), Expect = 2.0e-149, P = 2.0e-149
 Identities = 267/370 (72%), Positives = 325/370 (87%)

Query:     1 MSEKPICIADFEHYAKAFLGKSVYDYYKSGADEQQTLAENVAAFSRLKLYPRMXXXXXXX 60
             M  + +CI+D+E + ++ L KSVYDYY+SGA++Q+TLA+N+ AFSR KLYPRM       
Sbjct:     1 MLPRLVCISDYEQHVRSVLQKSVYDYYRSGANDQETLADNIQAFSRWKLYPRMLRNVADI 60

Query:    61 XXXXXXXGQKVSMPICVAATAMQCMAHADGEIATVRACRSMGTGMMLSSWATSSIEEVAQ 120
                    GQ+VSMPICV ATAMQCMAH DGE+ATVRAC++MGTGMMLSSWATSSIEEVA+
Sbjct:    61 DLSTSVLGQRVSMPICVGATAMQCMAHVDGELATVRACQTMGTGMMLSSWATSSIEEVAE 120

Query:   121 AAPEAVRWLQLYIYKDREVTKSLVRRAEKTGYKGIFVTVDTPFLGKRLDDVRNKFQLPPH 180
             A PEA+RW+QLYIYKDRE+++ +V+RAEK GYK IFVTVDTP+LG R+DDVRN+F+LPP 
Sbjct:   121 AGPEALRWMQLYIYKDREISRQIVKRAEKQGYKAIFVTVDTPYLGNRIDDVRNRFKLPPQ 180

Query:   181 LRMKNFETNDLAFSSEKGYGENSGLSVYVAEAIDPSINWEDMKWLRGLTSLPIVAKGIIR 240
             LRMKNFETNDLAFS +  +G+NSGL+ YVA+AIDPS++W+D+ WLR LTSLPIV KGI+R
Sbjct:   181 LRMKNFETNDLAFSPKGNFGDNSGLAEYVAQAIDPSLSWDDITWLRRLTSLPIVVKGILR 240

Query:   241 ADDAREAVKHGVNGILVSNHGARQLDGVPATIEILPEIIEAVEGKIEVFLDGGIRKGTDV 300
              DDA+EAVKHGV+GILVSNHGARQLDGVPATI++LPEI+EAVEGK+EVFLDGG+RKGTDV
Sbjct:   241 GDDAKEAVKHGVDGILVSNHGARQLDGVPATIDVLPEIVEAVEGKVEVFLDGGVRKGTDV 300

Query:   301 LKALALGARAVFLGRPIIWGLAYQGEQGVKEVLQILKEEFHLAMALSGCQSVEAIDRTLV 360
             LKALALGA+AVF+GRPIIWGLA+QGE+GV++VL+ILKEEF LAMALSGCQ+V+ ID+TLV
Sbjct:   301 LKALALGAKAVFVGRPIIWGLAFQGEKGVQDVLEILKEEFRLAMALSGCQNVKVIDKTLV 360

Query:   361 RREQWAASKM 370
             R+   A SK+
Sbjct:   361 RKNPLAVSKI 370