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Gene Model: Aco2

NomenclatureGenomic Location
SymbolAco2Chromosome2
NameAconitate hydratase, mitochondrialLinkage mapunknown
SpeciesDracomimus familiarisGenome Coordinates2: 87 Mbp

Molecular Function

Catalyzes the isomerization of citrate to isocitrate via cis-aconitate.

Citrate = isocitrate.

Molecular Function Terms:

binding
   ion binding
      cation binding
         metal ion binding
   metal cluster binding
      iron-sulfur cluster binding

catalytic activity
   lyase activity
      carbon-oxygen lyase activity
         hydro-lyase activity

Human Disease Association

No disease association.

Predicted Transcript
       ...................................ATGGCGCCGTACTGCGTCCTGGCGG
    26 CTCGGCTGCGGCATGCCCTGAATGGTGGGATACGGCGCTACCATGTTGCATCTGTTCTAT
    86 GCCAGCGGGCCAAGGTGGCCATGAGCCACTTTGAGCCTAATGAATACATAAACTATGAAA
   146 AGTTGGAGAAGAACATCAACATCGTCCGTAAGAGGCTTGACCGTCCTCTGACCTTATCTG
   206 AGAAGATTGTATATGGACACCTGGATGACCCAGCAAAACAGGAGATTGAGAGAGGCAAGA
   266 CCTATTTGCGCCTGCGGCCTGACCGTGTGGCCATGCAGGATGCCACTGCTCAGATGGCAA
   326 TGCTACAGTTCATCAGCAGCGGGCTGCCGAAAGTGGCCGTGCCTTCCACCATCCACTGTG
   386 ATCACCTCATAGAAGCTCAGTCAGGTGGTGAAAAGGATCTTCGAAGAGCCAAGGACATAA
   446 ACCAGGAGGTGTACAACTTTCTATCGACGGCTGGTGCCAAGTATGGAGTGGGATTCTGGA
   506 AACCTGGATCAGGAATCATTCACCAGATCATTCTGGAGAACTACTCCTACCCTGGGGTTA
   566 TGTTGATTGGCACAGACTCACACACCCCCAACGGAGGTGGCTTGGGAGGAATCTGCATTG
   626 GAGTGGGTGGAGCTGATGCTGTAGATGTCATGGCAGGAATCCCTTGGGAGCTCAAATGCC
   686 CAAAGGTTATTGGTGTAAAACTAACTGGGAAGCTTTCTGGCTGGAGTTCTCCTAAAGATG
   746 TGATCCTGAAAGTGGCTGGCATCCTCACTGTTAAGGGTGGAACAGGTGCCATCATCGAAT
   806 ACCATGGGCCTGGTGTGGATTCGATCTCTTGCACTGGAATGGCAACAATCTGTAACATGG
   866 GGGCTGAAATTGGAGCTACCACCTCAGTCTTCCCTTACAACACCCGGATGAAGAAATACC
   926 TGGGCAAGACTGGGCGAGCTGACATAGCTGCACTGGCAGATGAGTTCCAGCAATACTTGG
   986 TGCCAGATGCTGGTTGTCAGTACGACCAGGTGATAGAAATCAACCTCAGTGAGCTGAAGC
  1046 CACATATCAATGGACCTTTCACACCAGACCTGGCGCACCCTGTGTCAGATGTTGGTGCTG
  1106 TGGCAGAAAAGGAGGGCTGGCCTGTTGATATCAGAGTTGGCCTGATTGGCAGCTGCACCA
  1166 ACTCCAGCTATGAGGACATGGGACGCTCTGCAGCAGTGGCAAAGCAGGCACTGGCGCATG
  1226 GGTTGAAGTGCAAATCAAAGTTCACAATCACACCAGGCTCAGAGCAAATCCGTGCCACCA
  1286 TTGAAAGGGACGGTTACGCGCAAATCCTGCGAGACGTTGGAGGGCTGATTCTTGCCAATG
  1346 CTTGTGGGCCATGCATTGGCCAGTGGGACAGGAAGGACATAAAGAAAGGAGAGAAAAACA
  1406 CAATAGTTACGTCTTACAACCGGAATTTCACAGGTCGCAATGATGCCAACCCAGAGACTC
  1466 ACGCGTTTGTGACCTCCCCAGAGATTGTCACAGCCCTGTCCATTGCTGGTACTCTAAAAT
  1526 TTAACCCTGAGACAGATTTCCTGACAGGAGCAGATGGGAAGAAGTTTAAACTAGAAGCAC
  1586 CTGATGCAGATGAGCTGCCTAGGCTGGATTTTGACCCAGGCCAGGACACGTATCAGTACC
  1646 CTCCCAAGGATGGCAGTGGGCAGCATGTGGATGTGAGCCCCACCAGCCAGCGCCTCCAGC
  1706 TTCTTGAGCCCTTTGATAAGTGGGATGGCAAGGATCTAGAAGACATGCTGATCCTCATCA
  1766 AGGTAAAAGGGAAATGCACCACTGATCATATTTCTGCTGCTGGACCATGGCTCAAATTCC
  1826 GTGGCCATTTGGACAACATCTCCAACAACCTGCTCATTGGCGCTATCAACATTGAAAATG
  1886 GCAAAGCCAACTCTGTGAGGAATGCACTAACCCAGGAGTTTGGGCCTGTCCCAGACACAG
  1946 CCCGTTACTATAAGAAAATGGGTGTCAAATGGGCAGTTATTGGGGATGAAAACTATGGTG
  2006 AGGGATCAAGCCGAGAGCACGCAGCCTTGGAGCCACGTCACTTAGGGGGCAGGGTGATCA
  2066 TCACCAAGAGCTTTGCCAGGATCCACGAAACCAACCTGAAGAAGCAAGGTCTGCTGCCTC
  2126 TTACTTTTGCGGATCCAGCAGACTACAACAAGATTCATCCTGTGGACAAGCTGAGCATCG
  2186 TGGGGCTGGCAGACTTTGCTCCTGGAAAGCCTCTGAAATGCATCATCAAGCATCCCAACG
  2246 GGAGCCAAGAAACAATCATGTTGAACCACACCTTCAACGAGTCGCAGATCGAGTGGTTCC
  2306 AGGCTGGCAGTGCCCTGAACAGAATGAAGGAGCTGCAGCAGAAATCAAGCTAA

Predicted Protein Product
MAPYCVLAARLRHALNGGIRRYHVASVLCQRAKVAMSHFEPNEYINYEKLEKNINIVRKR
LDRPLTLSEKIVYGHLDDPAKQEIERGKTYLRLRPDRVAMQDATAQMAMLQFISSGLPKV
AVPSTIHCDHLIEAQSGGEKDLRRAKDINQEVYNFLSTAGAKYGVGFWKPGSGIIHQIIL
ENYSYPGVMLIGTDSHTPNGGGLGGICIGVGGADAVDVMAGIPWELKCPKVIGVKLTGKL
SGWSSPKDVILKVAGILTVKGGTGAIIEYHGPGVDSISCTGMATICNMGAEIGATTSVFP
YNTRMKKYLGKTGRADIAALADEFQQYLVPDAGCQYDQVIEINLSELKPHINGPFTPDLA
HPVSDVGAVAEKEGWPVDIRVGLIGSCTNSSYEDMGRSAAVAKQALAHGLKCKSKFTITP
GSEQIRATIERDGYAQILRDVGGLILANACGPCIGQWDRKDIKKGEKNTIVTSYNRNFTG
RNDANPETHAFVTSPEIVTALSIAGTLKFNPETDFLTGADGKKFKLEAPDADELPRLDFD
PGQDTYQYPPKDGSGQHVDVSPTSQRLQLLEPFDKWDGKDLEDMLILIKVKGKCTTDHIS
AAGPWLKFRGHLDNISNNLLIGAINIENGKANSVRNALTQEFGPVPDTARYYKKMGVKWA
VIGDENYGEGSSREHAALEPRHLGGRVIITKSFARIHETNLKKQGLLPLTFADPADYNKI
HPVDKLSIVGLADFAPGKPLKCIIKHPNGSQETIMLNHTFNESQIEWFQAGSALNRMKEL
QQKSS
Protein Alignment to Mouse
sp|Q99KI0|ACON_MOUSE Aconitate hydratase, mitochondrial OS=Mus musculus
            GN=Aco2 PE=1 SV=1
      MGI:87880 Aco2 aconitase 2, mitochondrial (Chr 15)
        Length = 780

 Score = 3759 (1328.3 bits), Expect = 0., P = 0.
 Identities = 706/782 (90%), Positives = 741/782 (94%)

Query:     1 MAPYCVLAARLRHALNGGIRRYHVASVLCQRAKVAMSHFEPNEYINYEKLEKNINIVRKR 60
             MAPY +L  RL+ AL  G+R+YHVASVLCQRAKVAMSHFEP+EYI Y+ LEKNINIVRKR
Sbjct:     1 MAPYSLLVTRLQKAL--GVRQYHVASVLCQRAKVAMSHFEPSEYIRYDLLEKNINIVRKR 58

Query:    61 LDRPLTLSEKIVYGHLDDPAKQEIERGKTYLRLRPDRVAMQDATAQMAMLQFISSGLPKV 120
             L+RPLTLSEKIVYGHLDDPA QEIERGKTYLRLRPDRVAMQDATAQMAMLQFISSGLPKV
Sbjct:    59 LNRPLTLSEKIVYGHLDDPANQEIERGKTYLRLRPDRVAMQDATAQMAMLQFISSGLPKV 118

Query:   121 AVPSTIHCDHLIEAQSGGEKDLRRAKDINQEVYNFLSTAGAKYGVGFWKPGSGIIHQIIL 180
             AVPSTIHCDHLIEAQ GGEKDLRRAKDINQEVYNFL+TAGAKYGVGFW+PGSGIIHQIIL
Sbjct:   119 AVPSTIHCDHLIEAQVGGEKDLRRAKDINQEVYNFLATAGAKYGVGFWRPGSGIIHQIIL 178

Query:   181 ENYSYPGVMLIGTDSHTPNXXXXXXXXXXXXXADAVDVMAGIPWELKCPKVIGVKLTGKL 240
             ENY+YPGV+LIGTDSHTPN             ADAVDVMAGIPWELKCPKVIGVKLTG L
Sbjct:   179 ENYAYPGVLLIGTDSHTPNGGGLGGICIGVGGADAVDVMAGIPWELKCPKVIGVKLTGSL 238

Query:   241 SGWSSPKDVILKVAGILTVKGGTGAIIEYHGPGVDSISCTGMATICNMGAEIGATTSVFP 300
             SGW+SPKDVILKVAGILTVKGGTGAI+EYHGPGVDSISCTGMATICNMGAEIGATTSVFP
Sbjct:   239 SGWTSPKDVILKVAGILTVKGGTGAIVEYHGPGVDSISCTGMATICNMGAEIGATTSVFP 298

Query:   301 YNTRMKKYLGKTGRADIAALADEFQQYLVPDAGCQYDQVIEINLSELKPHINGPFTPDLA 360
             YN RMKKYL KTGR DIA LA+EF+ +LVPD GCQYDQVIEINL+ELKPHINGPFTPDLA
Sbjct:   299 YNHRMKKYLSKTGRTDIANLAEEFKDHLVPDPGCQYDQVIEINLNELKPHINGPFTPDLA 358

Query:   361 HPVSDVGAVAEKEGWPVDIRVGLIGSCTNSSYEDMGRSAAVAKQALAHGLKCKSKFTITP 420
             HPV+DVG VAEKEGWP+DIRVGLIGSCTNSSYEDMGRSAAVAKQALAHGLKCKS+FTITP
Sbjct:   359 HPVADVGTVAEKEGWPLDIRVGLIGSCTNSSYEDMGRSAAVAKQALAHGLKCKSQFTITP 418

Query:   421 GSEQIRATIERDGYAQILRDVGGLILANACGPCIGQWDRKDIKKGEKNTIVTSYNRNFTG 480
             GSEQIRATIERDGYAQILRDVGG++LANACGPCIGQWDRKDIKKGEKNTIVTSYNRNFTG
Sbjct:   419 GSEQIRATIERDGYAQILRDVGGIVLANACGPCIGQWDRKDIKKGEKNTIVTSYNRNFTG 478

Query:   481 RNDANPETHAFVTSPEIVTALSIAGTLKFNPETDFLTGADGKKFKLEAPDADELPRLDFD 540
             RNDANPETHAFVTSPEIVTAL+IAGTLKFNPETDFLTG DGKKFKLEAPDADELPR DFD
Sbjct:   479 RNDANPETHAFVTSPEIVTALAIAGTLKFNPETDFLTGKDGKKFKLEAPDADELPRSDFD 538

Query:   541 PGQDTYQYPPKDGSGQHVDVSPTSQRLQLLEPFDKWDGKDLEDMLILIKVKGKCTTDHIS 600
             PGQDTYQ+PPKD SGQ VDVSPTSQRLQLLEPFDKWDGKDLED+ ILIKVKGKCTTDHIS
Sbjct:   539 PGQDTYQHPPKDSSGQRVDVSPTSQRLQLLEPFDKWDGKDLEDLQILIKVKGKCTTDHIS 598

Query:   601 AAGPWLKFRGHLDNISNNLLIGAINIENGKANSVRNALTQEFGPVPDTARYYKKMGVKWA 660
             AAGPWLKFRGHLDNISNNLLIGAINIENGKANSVRNA+TQEFGPVPDTARYYKK G++W 
Sbjct:   599 AAGPWLKFRGHLDNISNNLLIGAINIENGKANSVRNAVTQEFGPVPDTARYYKKHGIRWV 658

Query:   661 VIGDENYGEGSSREHAALEPRHLGGRVIITKSFARIHETNLKKQGLLPLTFADPADYNKI 720
             VIGDENYGEGSSREHAALEPRHLGGR IITKSFARIHETNLKKQGLLPLTFADP+DYNKI
Sbjct:   659 VIGDENYGEGSSREHAALEPRHLGGRAIITKSFARIHETNLKKQGLLPLTFADPSDYNKI 718

Query:   721 HPVDKLSIVGLADFAPGKPLKCIIKHPNGSQETIMLNHTFNESQIEWFQAGSALNRMKEL 780
             HPVDKL+I GL DFAPGKPLKC+IKHPNG+QETI+LNHTFNE+QIEWF+AGSALNRMKEL
Sbjct:   719 HPVDKLTIQGLKDFAPGKPLKCVIKHPNGTQETILLNHTFNETQIEWFRAGSALNRMKEL 778

Query:   781 QQ 782
             QQ
Sbjct:   779 QQ 780